Test Code HEMP Hereditary Erythrocytosis Mutations, Whole Blood
Profile Information
Test ID | Reporting Name | Available Separately | Always Performed |
---|---|---|---|
MINT | Molecular Interpretation | No | Yes |
EPOR | EPOR Gene, Mutation Analysis, B | No | Yes |
HIF2A | HIF2A Gene, Mutation Analysis, B | No | Yes |
PHD2 | PHD2 Gene, Mutation Analysis, B | No | Yes |
Testing Algorithm
This evaluation is recommended for patients presenting with lifelong erythrocytosis, usually with a positive family history of similar symptoms. Polycythemia vera should be excluded prior to testing as it is much more common than hereditary erythrocytosis and can be present even in young patients. A JAK2 V617F or JAK2 exon 12 variant should not be present. Additionally, testing to exclude the possibility of a high oxygen affinity hemoglobin variant should be performed before ordering this test. See Ordering Guidance.
Additional testing for BPGM full gene sequencing and VHL gene erythrocytosis variant analysis will always be performed at an additional charge.
For more information see Erythrocytosis Evaluation Testing Algorithm
Performing Laboratory
Mayo Clinic Laboratories in RochesterSpecimen Type
Whole bloodOrdering Guidance
For a complete evaluation including hemoglobin electrophoresis testing and hereditary erythrocytosis variant analysis in an algorithmic fashion, order REVE2 / Erythrocytosis Evaluation, Blood.
This test does not provide a serum erythropoietin (EPO) level. If EPO testing is desired, order EPO / Erythropoietin, Serum.
Necessary Information
Erythrocytosis Patient Information (T694) is strongly recommended, but not required, to be filled out and sent with the specimen. This information aids in providing a more thorough interpretation of test results. Ordering providers are strongly encouraged to complete the form and send it with the specimen.
Specimen Required
Container/Tube: Lavender top (EDTA)
Specimen Volume: 3 mL
Collection Instructions: Send whole blood specimen in original tube. Do not aliquot.
Specimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Whole blood | Refrigerated (preferred) | 30 days | |
Ambient | 14 days |
Special Instructions
Reference Values
An interpretive report will be provided.
Day(s) Performed
Monday through Friday
CPT Code Information
81479
Report Available
10 to 25 daysReject Due To
Gross hemolysis | Reject |
Gross lipemia | Reject |
Gross icterus | Reject |
Moderately to severely clotted | Reject |
Method Name
Polymerase Chain Reaction (PCR) Amplification/Sanger Sequence Analysis
Forms
1. New York Clients-Informed consent is required. Document on the request form or electronic order that a copy is on file. The following documents are available in Special Instructions:
-Informed Consent for Genetic Testing (T576)
-Informed Consent for Genetic Testing-Spanish (T826)
2. Erythrocytosis Patient Information (T694)
3. If not ordering electronically, complete, print, and send a Benign Hematology Test Request Form (T755) with the specimen.
Secondary ID
61337Additional Tests
Test ID | Reporting Name | Available Separately | Always Performed |
---|---|---|---|
BPGMM | BPGM Full Gene Sequencing | Yes | Yes |
VHLE | VHL Gene Erythrocytosis Mutations | No, (Order VHLZZ) | Yes |