Test Code AAPD Amino Acids, Quantitative, Random, Urine
Performing Laboratory
Mayo Clinic Laboratories in RochesterSpecimen Type
UrineAdditional Testing Requirements
Not all patients with homocystinuria will be detected by this assay. If homocystinuria is a concern, order CMMPP / Cobalamin, Methionine, and Methylmalonic Acid Pathways, Plasma or HCYSP / Homocysteine, Total, Plasma or HCYSS / Homocysteine, Total, Serum in tandem with this test.
Necessary Information
1. Patient's age is required.
2. Include family history, clinical condition (asymptomatic or acute episode), diet, and drug therapy information.
3. If prolidase deficiency is a concern, indicate on the amino acid order "Pretreat with acid hydrolysis prior to analysis". The acid hydrolysis will break up in vitro proline and hydroxyproline containing dipeptides, which are cleaved in vivo by prolidase.
Specimen Required
Supplies: Urine Tubes, 10 mL (T068)
Specimen Volume: 2 mL
Collection Instructions: Collect a random urine specimen.
Specimen Minimum Volume
1 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Frozen (preferred) | 70 days | |
Refrigerated | 14 days |
Reference Values
Amino Acid |
Age groups |
|||||
< 2 months |
2-35 months |
3-6 years |
7-17 years |
≥18 years |
||
Taurine |
Tau |
<9026 |
<5604 |
<3680 |
<3954 |
<2134 |
Asparagine |
Asn |
<687 |
<1159 |
<238 |
<322 |
<204 |
Serine |
Ser |
<3202 |
<2741 |
<1386 |
<1116 |
<658 |
Hydroxyproline |
Hyp |
<2254 |
<1775 |
<89 |
<42 |
<48 |
Glycine |
Gly |
<13336 |
<9872 |
<4997 |
<4467 |
<4068 |
Glutamine |
Gln |
<2931 |
<3681 |
<1124 |
<1038 |
<764 |
Aspartic Acid |
Asp |
<290 |
<72 |
<46 |
<13 |
<12 |
Ethanolamine |
EtN |
<1589 |
<1765 |
<776 |
<536 |
<500 |
Histidine |
His |
<3806 |
<4578 |
<2596 |
<2294 |
<1508 |
Threonine |
Thr |
<1930 |
<1769 |
<496 |
<575 |
<384 |
Citrulline |
Cit |
<61 |
<67 |
<23 |
<17 |
<34 |
Sarcosine |
Sar |
<177 |
<52 |
<6 |
<10 |
<6 |
Beta-Alanine |
bAla |
<174 |
<79 |
<99 |
<139 |
<58 |
Alanine |
Ala |
<2856 |
<2360 |
<961 |
<794 |
<472 |
Glutamic Acid |
Glu |
<281 |
<210 |
<127 |
<63 |
<62 |
1-Methylhistidine |
1MHis |
<493 |
<470 |
<517 |
<453 |
<265 |
3-Methylhistidine |
3MHis |
<196 |
<662 |
<3346 |
<2027 |
<1920 |
Argininosuccinic Acid |
Asa |
<96 |
<103 |
<65 |
<57 |
<37 |
Homocitrulline |
Hcit |
<164 |
<169 |
<110 |
<107 |
<87 |
Arginine |
Arg |
<250 |
<147 |
<81 |
<42 |
<65 |
Alpha-aminoadipic Acid |
Aad |
<264 |
<397 |
<349 |
<138 |
<73 |
Gamma Amino-n-butyric Acid |
GABA |
<8 |
<14 |
<4 |
<3 |
<4 |
Beta-aminoisobutyric Acid |
bAib |
<2214 |
<2488 |
<840 |
<251 |
<265 |
Alpha-amino-n-butyric Acid |
Abu |
<58 |
<44 |
<37 |
<29 |
<19 |
Hydroxylysine |
Hyl |
<101 |
<87 |
<44 |
<22 |
<16 |
Proline |
Pro |
<1776 |
<1028 |
<29 |
<42 |
<98 |
Ornithine |
Orn |
<344 |
<238 |
<228 |
<291 |
<193 |
Cystathionine |
Cth |
<118 |
<53 |
<23 |
<24 |
<33 |
Cystine |
Cys |
<486 |
<285 |
<111 |
<84 |
<142 |
Lysine |
Lys |
<2217 |
<1321 |
<814 |
<463 |
<295 |
Methionine |
Met |
<76 |
<45 |
<24 |
<22 |
<15 |
Valine |
Val |
<308 |
<258 |
<119 |
<91 |
<73 |
Tyrosine |
Tyr |
<453 |
<603 |
<289 |
<371 |
<155 |
Isoleucine |
Ile |
<99 |
<131 |
<52 |
<29 |
<26 |
Leucine |
Leu |
<286 |
<215 |
<87 |
<70 |
<64 |
Phenylalanine |
Phe |
<342 |
<306 |
<178 |
<123 |
<98 |
Tryptophan |
Trp |
<241 |
<329 |
<222 |
<218 |
<140 |
Allo-isoleucine |
AlloIle |
<3 |
<6 |
<1 |
<2 |
<4 |
All results reported as nmol/mg creatinine.
Day(s) Performed
Monday through Friday
CPT Code Information
82139
Report Available
3 to 5 daysReject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Testing Algorithm
Testing includes quantitation of the following amino acids: taurine, threonine, serine, asparagine, hydroxyproline, glutamic acid, glutamine, aspartic acid, ethanolamine, sarcosine, proline, glycine, alanine, citrulline, alpha-aminoadipic acid, alpha-amino-n-butyric acid, valine, cystine, cystathionine, methionine, isoleucine, leucine, tyrosine, phenylalanine, beta-alanine, beta-aminoisobutyric acid, ornithine, lysine, 1-methylhistidine, histidine, 3-methylhistidine, argininosuccinic acid, allo-isoleucine, homocitrulline, gamma-amino-n-butyric acid, hydroxylysine, tryptophan, and arginine.
Method Name
Liquid Chromatography Tandem Mass Spectrometry (LC-MS/MS)
Portions of this test are covered by patents held by Quest Diagnostics
Forms
If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.